Medical Definition of ATP cobalamin adenoxyltransferase
1. 
 An enzyme that catalyses the reaction of ATP, water, and cobalamin to form orthophosphate, pyrophosphate, and adenoxylcobalamin. Adenosylcobalamin is required by methylmalonyl-CoA mutase. A deficiency of ATP cobalamin adenosyltransferase will lead to methylmalonic acidemia.
(05 Mar 2000)
 
Lexicographical Neighbors of ATP Cobalamin Adenoxyltransferase
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