Medical Definition of Lysosomal storage diseases

1. Inborn errors of metabolism characterised by defects in specific lysosomal hydrolases and resulting in intracellular accumulation of unmetabolised substrates. (12 Dec 1998)

Lexicographical Neighbors of Lysosomal Storage Diseases

lysophosphatidic acid
lysophosphatidic acid-hydrolysing lysophospholipase
lysophosphatidic acid acyltransferase
lysophosphatidic acid phosphatase
lysophosphatidylcholine
lysophosphatidylcholines
lysophosphatidylserine
lysophospholipase
lysophospholipase-transacylase
lysophospholipids
lysosogenic bacteriophage
lysosomal
lysosomal disease
lysosomal diseases
lysosomal enzyme
lysosomal storage diseases (current term)
lysosome
lysosome
lysosomes
lysosomes
lysosome associated membrane glycoprotein
lysosome phagosome fusion
lysostaphin
lysostaphin endopeptidase
lysotype
lysozyme
lysozyme
lysozymes
lyssa
lyssa

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